| SPECIESREACTIVITY: | Human |
|---|---|
| TESTEDAPPLICATIONS: | ELISA,WB |
| APPLICATIONS: | ELISA:antibodydetectionlimitdilution1:32000.WesternBlot:Preliminaryexperimentsgaveanapprox.50kDabandinHumanBrain(Cerebellum)lysatesafter1μg/mlantibodystaining.Pleasenotethatcurrentlywecannotfindanexplanationintheliteratureforthebandweobservegiventhecalculateds |
| POSITIVECONTROL: | 1)Cat.No.1210-293CellLysate |
| IMMUNOGEN: | ABCD1antibodywasraisedagainsta12aminoacidsyntheticpeptideneartheinternalregionofABCD1. |
| HOSTSPECIES: | Goat |
| PURIFICATION: | ABCD1antibodywaspurifiedfromgoatserumbyammoniumsulphateprecipitationfollowedbyantigenaffinitychromatographyusingtheimmunizingpeptide. |
|---|---|
| PHYSICALSTATE: | Liquid |
| BUFFER: | ABCD1antibodyissuppliedinTrissaline,0.02%sodiumazide,pH7.3with0.5%bovineserumalbumin. |
| CONCENTRATION: | 500ug/mL |
| STORAGECONDITIONS: | Aliquotandstoreat-20˚C.Minimizefreezingandthawing. |
| CLONALITY: | Polyclonal |
| CONJUGATE: | Unconjugated |
| ALTERNATENAMES: | ABCD1,ATP-bindingcassette,sub-familyD(ALD),member1,ABC42,ALD,ALDP,AMN,adrenoleukodystrophyprotein |
|---|---|
| ACCESSIONNO.: | NP_000024.2 |
| PROTEINGINO.: | 7262393 |
| OFFICIALSYMBOL: | ABCD1 |
| GENEID: | 215 |
| REFERENCES: | 1)HöftbergerR,KunzeM,WeinhoferI,Aboul-EneinF,VoigtländerT,OezenI,AmannG,BernheimerH,BudkaH,BergerJ.Distributionandcellularlocalizationofadrenoleukodystrophyproteininhumantissues:implicationsforX-linkedadrenoleukodystrophy.NeurobiolDis.2007Nov;28(2):165-74 |
|---|
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